King Kopetzky Syndrome

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The king-kopetzky syndrome refers to a hearing disorder that is characterized by the difficulty despite normal hearing threshold language to understand when there is background noise. King Kopetzky syndrome is counted among the auditory processing and perception disorders (AVWS).

Patients with King-Kopetzky syndrome describe hearing impairments in speech comprehension (especially when there is background noise) and show abnormal values ​​in the “Social Hearing Handicap index” (SHHI) with normal or only slightly deviating results in all common hearing tests. Although the syndrome was described by Samuel J. Kopetzky as early as 1948 and further investigated by P. F. King in 1954, it is still little known in German-speaking countries. Nevertheless, up to 10% of all patients who see a doctor for hearing problems are said to suffer from it.

causes

The causes of King Kopetzky syndrome have not yet been conclusively researched. However, there is increasing evidence that King-Kopetzky patients suffer from neuropsychiatric abnormalities such as a. Suffer from anxiety disorders and obsessionality . Investigations into familial cluster formation point to hereditary factors (autosomal dominant) that contribute to the development of King-Kopetzky syndrome and possibly also neuropsychiatric abnormalities.

treatment

After other reasons for the hearing impairment have been ruled out, King-Kopetzky syndrome can be resolved through targeted hearing training , stress reduction, sound amplification systems (e.g. in classrooms), treatment of any neurological symptoms that may be present and, if there is measurable hearing loss in the audio audiogram , im If necessary, they can also be treated with the use of hearing aids .

Individual evidence

  1. ^ E. Borg, D. Stephens: King-Kopetzky syndrome in the light of an ecological conceptual framework . In: Int J Audiol . tape 42 , no. 6 , September 2003, p. 312-318 , doi : 10.3109 / 14992020309101323 , PMID 14570238 .
  2. ^ A b D. Stephens, F. Zhao: The role of a family history in King Kopetzky Syndrome (obscure auditory dysfunction) . In: Acta Otolaryngol . tape 120 , no. 2 , March 2000, p. 197-200 , doi : 10.1080 / 000164800750000900 , PMID 11603771 .
  3. ^ A b F. Zhao, D. Stephens: Determinants of speech-hearing disability in King-Kopetzky syndrome . In: Scand Audiol . tape 25 , no. 2 , 1996, p. 91-96 , PMID 8738633 .
  4. ↑ Is there an association between noise exposure and King Kopetzky Syndrome? In: Noise and Health .
  5. ↑ Helen Pryce, Chris Metcalfe, Lindsay St Claire, Amanda Hall: Causal attributions in King-Kopetzky syndrome. In: International journal of audiology. 04/2010, 49 (7), pp. 482-487. doi: 10.3109 / 14992021003682319 .
  6. ↑ K. King, D. Stephens: Auditory and psychological factors in 'auditory disability with normal hearing' . In: Scand Audiol . tape 21 , no. 2 , 1992, p. 109-114 , PMID 1641572 .
  7. ↑ Dafydd Stephens, Fei Zhao: The Role of a Family History in King Kopetzky Syndrome (Obscure Auditory Dysfunction). In: Acta Oto-laryngologica. 2000, vol. 120, no. 2, pp. 197-200. doi: 10.1080 / 000164800750000900 .
  8. ↑ XZ Liu, L. Xu, V. Newton: Audiometric configuration in non-syndromic genetic hearing loss . In: J Audiol Med . tape 3 , p. 99-106 .
  9. ↑ G. Van Camp, PJ Willems, RJH Smith: Non-syndromic hearing impairment: unparalleled heterogeneity . In: Am J Genet . tape 60 , 1997, pp. 758-764 .
  10. ^ Helen Pryce: Managing King-Kopetzky Syndrome. (PDF) Thesis . Health University of Bath School for Health, February 2009.
  11. ↑ American Academy of Audiology: Clinical Practice Guidelines: Diagnosis, Treatment and Management of Children and Adults with Central Auditory Processing Disorder (PDF)