Café-au-lait spot
| Classification according to ICD-10 | |
|---|---|
| L81.3 | Café-au-lait spots |
| ICD-10 online (WHO version 2019) | |
Café-au-lait spots (from French café au lait = " milk coffee ") are light brown, even skin spots of different sizes that can appear in different numbers on the whole body. Since it is a sharply demarcated, benign skin lesion ( nevus ), the term nevus pigmentosus is sometimes used, but this should not be confused with the general term pigment nevus for pigmented nevi .
Appearance
Café-au-lait stains have a light to dark brown, absolutely even pigmentation. Their size can vary widely, from under 2 mm to over 20 cm. They typically appear on the extremities or trunk. In contrast to other pigment nevi, they are never raised or knotty and are not associated with hypertrichosis .
meaning
Café-au-lait stains are not a disease. 10–20% of the normal population have one or more of these homogeneous hyperpigmentations . An increased occurrence is described in vitamin B 12 deficiency , neurofibromatosis ( Recklinghausen's disease ), Fanconi anemia and McCune-Albright syndrome . If more than six café-au-lait spots with a diameter greater than 15 mm in adulthood or greater than 5 mm in children and adolescents, and the appearance of further symptoms, the diagnosis of neurofibromatosis type 1 is likely. These café-au-lait spots are typically smooth ( Coast of California ), while in McCune-Albright syndrome they appear irregularly bordered ( Coast of Maine or Coast of Massachusetts ).
literature
- Thomas B. Fitzpatrick, Klaus Wolff (ed.): Atlas and synopsis of clinical dermatology: common and threatening diseases . 3. Edition. McGraw-Hill, New York / Frankfurt a. M. 1998, ISBN 0-07-709988-5 .
- Ernst G. Jung, Ingrid Moll (Ed.): Dermatology . 5th edition. Thieme, Stuttgart 2003, ISBN 3-13-126685-6
Individual evidence
- ↑ Dr. Alice Martin: Skin Lexicon: Café-au-lait spots - Symptoms. Dermanostic, accessed May 19, 2020 .
- ↑ ncbi.nlm.nih.gov MedGen, Fanconi Anemia
