Neuralgic amyotrophy
| Classification according to ICD-10 | |
|---|---|
| G54.5 | Neuralgic amyotrophy |
| ICD-10 online (WHO version 2019) | |
The neuralgic amyotrophy is a very rare disease of the peripheral nerves with violent pain and muscle weakness to muscle atrophy in the upper extremities and slow recovery for months to years.
There are two forms to be distinguished:
- idiopathic form (INA) , s. Neuralgic shoulder amyotrophy
- hereditary form (HNA) , s. Hereditary neuralgic amyotrophy
The first description comes from 1960 by RA Taylor.
distribution
The frequency is given as 1–5 in 10,000.
Clinical manifestations
The disease can occur at any age, more often in men than in women, the congenital form earlier than the idiopathic form, otherwise there are no clinical differences.
Differential diagnosis
The following are to be distinguished:
literature
- P. Seror: Neuralgic amyotrophy. To update. In: Joint, bone, spine: revue du rhumatisme. Volume 84, number 2, March 2017, pp. 153-158, doi: 10.1016 / j.jbspin.2016.03.005 , PMID 27263426 (review).
- JJ Van Eijk, JT Groothuis, N. Van Alfen: Neuralgic amyotrophy: An update on diagnosis, pathophysiology, and treatment. In: Muscle & nerve. Volume 53, Number 3, March 2016, pp. 337-350, doi: 10.1002 / mus.25008 , PMID 26662794 (review).
Individual evidence
- ↑ a b c d Neuralgic amyotrophy. In: Orphanet (Rare Disease Database).
- ^ RA Taylor: Heredofamilial mononeuritis multiplex with brachial predilection. In: Brain: a journal of neurology. Volume 83, March 1960, pp. 113-137, PMID 13837190 .
