Agastrie
| Classification according to ICD-10 | |
|---|---|
| Q40.2 | Other specified congenital malformations of the stomach - micro gastric disease |
| ICD-10 online (WHO version 2019) | |
The Agastrie from ancient Greek ἀ (ν) - a-, additions , German , negation un-, without (Alpha privativum) ' and ancient Greek γαστήρ gaster , German , stomach' , is a complete absence of the stomach , either as rare extremely congenital malformation or after surgical removal ( gastrectomy ).
The congenital form is based on a disturbance in embryonic development from about the 5th fetal week. As a rule, this disorder is associated with other malformations.
If part of the stomach is still in place, it is called micro gastric gastric disease .
The first description comes from 1987 by the Australian pediatrician SF Dorney and colleagues.
Clinical manifestations, diagnosis and therapy correspond to those described under micro gastric disease.
Individual evidence
- ↑ W. Schuster, D. Färber (editor): Children's radiology. Imaging diagnostics. 2nd edition, Springer 1996, Vol. II, p. 451, ISBN 3-540-60224-0 .
- ↑ Enrico Ganz
- ↑ CA Cuadros-Mendoza, MC Martínez-Soto, FE Zarate-Mondragón, R. Cervantes-Bustamante, JA Ramírez-Mayans: Congenital agastria as an isolated malformation. In: Revista de gastroenterologia de Mexico. Volume 84, number 2, 2019 Apr - Jun, pp. 257-259, doi: 10.1016 / j.rgmx.2018.04.004 , PMID 29941238 .
- ^ SF Dorney, AW Middleton, K. Kozlowski, BN Benjamin, AE Kan, KR Kamath: Congenital agastria. In: Journal of Pediatric Gastroenterology and Nutrition . Volume 6, Number 2, 1987 Mar-Apr, pp. 307-310, doi: 10.1097 / 00005176-198703000-00026 , PMID 3694355 .
