Aminoaciduria

Classification according to ICD-10
E72.9	Disorder of amino acid metabolism, unspecified
ICD-10 online (WHO version 2019)

Amino aciduria is the excretion of amino acids in the urine . Small amounts of amino acids can also occur in healthy people.

One pathology is the increased excretion of amino acids in the urine and is called hyperaminoaciduria , although both terms are often used synonymously. It is considered increased when more than 5% of the glomerularly filtered amino acids are not reabsorbed but are excreted.

Classification

Prerenal forms

• in hyperaminoacidemia (increased amount of protein in the blood)
  • without inhibiting specific transport systems, e.g. B. in phenylketonuria
  • with inhibition of group-specific transport systems, e.g. B. by imino acids or dibasic amino acids
• with reduced tubular reabsorption z. B. in beta-amino-isobutyric acid, homocystinuria

Renal forms

• Disturbance of the individual specific transport systems, e.g. B. in hypercystinuria , hyperglycinuria
• Disruption of the group-specific transport systems, e.g. B. in cystinuria , dibasic hyperaminoaciduria, Hartnup disease , iminoglycinuria

Generalized forms

• primarily for inherited disorders
• secondary to acquired disorders

Individual evidence

1. ↑ ^{a b} W. Pschyrembel: Clinical Dictionary. Verlag Walter de Gruyter, 265th edition (2014), ISBN 3-11-018534-2 , p. 733.
2. ↑ Entry on amino aciduria in the Flexikon , a Wiki of the DocCheck company

This article is about a health issue. It is not used for self-diagnosis and does not replace a diagnosis by a doctor. Please note the information on health issues !