Microcolon

from Wikipedia, the free encyclopedia
Classification according to ICD-10
Q43.8 Other specified congenital malformations of the intestine - including: microcolon
ICD-10 online (WHO version 2019)

A microcolon , from ancient Greek μικρός mikrós , German 'small, narrow' and ancient Greek κῶλον kōlon , German 'gut, sausage' , is an abnormally small, unfilled large intestine ( colon ), usually due to insufficient use. It is an indication of an intrauterine disturbed meconium passage into the large intestine and usually occurs in the case of (congenital) obstructions in the passage of the gastrointestinal tract.

causes

Common causes are:

As part of some syndromes , the microcolon can be an essential feature:

diagnosis

The diagnosis is made by a colonic enema . The colon is underdeveloped, as thick as a finger, thin-walled, shorter than normal and has hardly any flexures.

Differential diagnosis

The neonatal small left colon syndrome , consequences of necrotizing enterocolitis , meconium plug syndrome , functional microcolon in premature infants are to be distinguished.

literature

  • A. Saskin, A. Alfares, C. Bernard, M. Blumenkrantz, N. Braverman, I. Gupta, KB Brosnihan, C. Antignac, MC Gubler, V. Morinière, I. De Bie, M. Bitzan: Renal tubular dysgenesis and microcolon, a novel association. Report of three cases. In: European journal of medical genetics. Volume 62, number 4, April 2019, pp. 254-258, doi: 10.1016 / j.ejmg.2018.07.024 , PMID 30071301 .
  • S. Armbrust, R. Hoffmann, F. Jochum, LM Neumann, C. Fusch: Restrictive dermopathy associated with transposition of the great arteries and microcolon: a rare neonatal entity with new symptoms. In: Archives of dermatology. Volume 141, Number 5, May 2005, pp. 611-613, doi: 10.1001 / archderm.141.5.611 , PMID 15897383 .
  • LF Donnelly, JF Johnson: Case report: inverted Meckel's diverticulum with associated microcolon. In: Clinical radiology. Volume 53, Number 3, March 1998, pp. 226-227, doi: 10.1016 / s0009-9260 (98) 80107-4 , PMID 9528877 .
  • JC Leonidas: Microcolon in the absence of small bowel obstruction in the newborn. In: Journal of pediatric surgery. Volume 24, Number 2, February 1989, pp. 180-182, doi: 10.1016 / s0022-3468 (89) 80244-1 , PMID 2656971 .
  • Marcel Bettex (ed.), Max Grob (introductory), D. Berger (editing), N. Genton, M. Stockmann: Pediatric Surgery. Diagnostics, indication, therapy, prognosis. 2nd, revised edition, Thieme, Stuttgart / New York 1982, ISBN 3-13-338102-4

Individual evidence

  1. ↑ a b c W. Schuster, D. Färber (editor): Children's radiology. Imaging diagnostics. Springer 1996, 2nd edition, p. 588, ISBN 3-540-60224-0 .
  2. ↑ Radiopaedia
  3. ↑ J. Amodio, W. Berdon, S. Abramson, C. Stolar: Microcolon of prematurity: a form of functional obstruction. In: American Journal of Roentgenology . Volume 146, Number 2, February 1986, pp. 239-244, doi: 10.2214 / ajr.146.2.239 , PMID 3484569 .
  4. ↑ Bernfried Leiber (founder): The clinical syndromes. Syndromes, sequences and symptom complexes . Ed .: G. Burg, J. Kunze, D. Pongratz, PG Scheurlen, A. Schinzel, J. Spranger. 7., completely reworked. Edition. tape 2 : symptoms . Urban & Schwarzenberg, Munich et al. 1990, ISBN 3-541-01727-9 .
  5. ↑ Megacystis-microcolon-intestinal hypoperistalsis syndrome. In: Orphanet (Rare Disease Database).
  6. ↑ WE Berdon, DH Baker, WA Blanc, B. Gay, TV Santulli, C. Donovan: megacystis-micro-colon intestinal hypoperistalsis syndrome: a new cause of intestinal obstruction in the newborn. Report of radiological findings in five newborn girls. In: American Journal of Roentgenology . Volume 126, Number 5, May 1976, pp. 957-964, doi: 10.2214 / ajr.126.5.957 , PMID 178239 .
  7. ↑ Microcolon.  In: Online Mendelian Inheritance in Man . (English)
  8. ↑ IH Krasna, D. Rosenfeld, P. Salerno: Is it necrotizing enterocolitis, microcolon of prematurity, or delayed meconium plug? A dilemma in the tiny premature infant. In: Journal of pediatric surgery. Volume 31, Number 6, June 1996, pp. 855-858, doi: 10.1016 / s0022-3468 (96) 90153-0 , PMID 8783123 .