Palmar syndrome

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Classification according to ICD-10
Q27.8 Other specified congenital malformations of the peripheral vasculature
ICD-10 online (WHO version 2019)

The Palmar syndrome is a very rare congenital disease with a symmetrical, chronic erythema of the palms and soles.

Synonyms are: disease of the red palms; Red palatine syndrome; Latin Erythema palmoplantare hereditarium; Erythema palmar hereditarium; Erythema palmo-plantare ; Maladie de v. Bechterew-Stoelzner; English Lane's Disease

The name refers to the author of the first description from 1929 by John E. Lane .

distribution

The frequency is unknown; the inheritance is autosomal dominant .

root cause

The disease is based on a disturbance of the palmo-plantar blood flow due to a dysplasia of the skin vessels with a strong increase and anastomosis of the capillaries .

Clinical manifestations

Clinical criteria are:

Chronic, extensive erythema of 4 to 10 cm in size without complaints, mainly on the heels of the hand, but also on the fingers. The palm and back of the hand are spared.

Differential diagnosis

Acquired palmar erythema must be distinguished .

literature

  • M. Durieux-Verde, D. Raffin, C. Dannepond, A. Maruani: Érythème palmaire héréditaire (maladie de Lane): observation chez un enfant. In: Annales de dermatologie et de venereologie , Volume 143, No. 1, January 2016, pp. 32-35, doi: 10.1016 / j.annder.2015.10.578 , PMID 26563821 (Review).
  • J. Langenauer: Erythema Palmare Hereditarium ('Red Palms', 'Lane's Disease'). In: Case reports in dermatology , Volume 6, No. 3, September 2014, pp. 245-247, doi: 10.1159 / 000368822 , PMID 25493079 , PMC 4255997 (free full text).
  • RA Rupec, H. Wolff, A. Lindner, P. Child: Erythema palmare hereditarium (“red palms”). In: The dermatologist ; Journal of Dermatology, Venereology, and Related Fields , Volume 51, No. 4, April 2000, pp. 264-265, PMID 10810663 .

Web links

Individual evidence

  1. ↑ a b Bernfried Leiber (founder): The clinical syndromes. Syndromes, sequences and symptom complexes . Ed .: G. Burg, J. Kunze, D. Pongratz, PG Scheurlen, A. Schinzel, J. Spranger. 7., completely reworked. Edition. tape 2 : symptoms . Urban & Schwarzenberg, Munich et al. 1990, ISBN 3-541-01727-9 .
  2. ↑ a b Erythema palmar hereditarium. In: Orphanet (Rare Disease Database).
  3. ↑ JE Lane: Erythema palmar hereditarium (red palms). In: Archives of Dermatology and Syphilology (Chicago), Volume 20, 1929, pp. 445-448
  4. ↑ a b Encyclopedia Dermatology