Aortic arch syndrome
| Classification according to ICD-10 | |
|---|---|
| M31.4 | Aortic arch syndrome [Takayasu syndrome] |
| Q25.4 | Other congenital malformations of the aorta |
| ICD-10 online (WHO version 2019) | |
The aortic arch syndrome (synonyms: Mangold-Roth disease, Pulseless disease, pulseless disease, obliteration syndrome [of the supra-aortic vessels], Takayasu syndrome) is caused by the occlusion or partial occlusion of one or more vessels that branch off from the aortic arch .
causes
The aortic arch syndrome first described by the Japanese ophthalmologist Takayasu in 1908 can be due to both arteriosclerosis and inflammation-related occlusions of blood vessels. The most common causes are the Takayasu arteritis , arteriosclerosis , endangiitis obliterans and congenital malformations .
clinic
Typically, the upper extremities show decreased blood pressure or lack of pulse, and the lower extremities show increased blood pressure (hypotension) due to reduced blood flow to the carotid artery (with the functionally impaired blood pressure sensor in the carotid sinus) (in the case of aortic isthmus syndrome , the opposite is true). Possible consequences of reduced blood flow in the head area are cerebellar and hemisphere symptoms, syncope , visual disturbances, inner ear disturbances , trophic disturbances in the hands and face, as well as chewing problems ( claudication ).
therapy
Therapeutic options are thrombus endarterectomy , bypass anastomoses and reconstructive plastic surgery .
Individual evidence
- ^ Klaus Holldack, Klaus Gahl: Auscultation and percussion. Inspection and palpation. Thieme, Stuttgart 1955; 10th, revised edition, ibid 1986, ISBN 3-13-352410-0 , p. 219.
- ^ Klaus Holldack, Klaus Gahl: Auscultation and percussion. Inspection and palpation. 1986, p. 219.
