Fuchs heterochromic iridocyclitis
| Classification according to ICD-10 | |
|---|---|
| H20.1 | Chronic iridocyclitis |
| H20.8 | Other iridocyclitis |
| ICD-10 online (WHO version 2019) | |
The Fuchs heterochromic iridocyclitis or Fuchs Syndrome III denotes a color difference between the iris of the right and left eyes ( iris Heterochromie ) together with a chronic inflammation of the iris of the lighter eye.
Synonyms are:
- Heterochromic Fuchs cyclitis
- Heterochromic cyclitis
- Heterochromia fox
- Fuchs' uveitis syndrome
- Fuchs heterochromic cyclitis
The name refers to the first description from 1904 by Weill and then in 1906 by the Austrian ophthalmologist Ernst Fuchs .
Epidemiology and cause
The frequency is given as 1–9: 1,000,000. The cause has not yet been clarified.
Clinical manifestations
Clinical criteria are:
- Diffuse heterochromia in non-irritating eyes or atrophy of the iris
- chronic mostly unilateral iridocyclitis on the side of the lighter iris
- keratitic deposits in the absence of synechia
In addition, glaucoma and vitreous opacities can develop .
Differential diagnosis
The following are to be distinguished:
- Posner-Schlossman syndrome
- Klein-Waardenburg syndrome
- Heterochromia simplex
- Uveitis
- Iris heterochromia in melanosis bulbi
Individual evidence
- ↑ a b c B. Leiber: The clinical syndromes. Syndromes, sequences and symptom complexes. Edited by G. Burg, J. Kunze, D. Pongratz, PG Scheurlen, A. Schinzel, J. Spranger, 7th edition. Urban & Schwarzenberg 1990, ISBN 3-541-01727-9
- ↑ E. Fuchs: About complications of heterochromia. In: Zeitschrift für Augenheilkunde , Basel, 1906, Vol. 15, pp. 191–212.
- ↑ a b Fuchs heterochromic iridocyclitis. In: Orphanet (Rare Disease Database).
