Nerve sheath tumor
Classification according to ICD-10 | |
---|---|
D36 | Benign neoplasm in other and unspecified locations |
D36.1 | Peripheral nerves and autonomic nervous system |
C76 | Malignant neoplasm in other and imprecisely designated locations |
ICD-10 online (WHO version 2019) |
Nerve sheath tumors are tumors that presumably originate from cells in the medullary sheaths and soft tissues surrounding the nerves . The most common benign nerve sheath tumor is the neurinoma . Neurofibromas , perineuriomas, and nerve sheath myxomas are less common . A malignant nerve sheath tumor is the malignant peripheral nerve sheath tumor (MPNST).
Nerve sheath tumors can occur sporadically or (more rarely) in connection with genetic diseases such as neurofibromatosis type 1 , neurofibromatosis type 2 , familial schwannomatosis and the Carney complex .
literature
- WHO Classification of Tumors of the Central Nervous System. (Eds. Cavenee, Louis, Ohgaki & Wiestler) Lyon, IARC Press, 2007, ISBN 9283224302