Pseudo-Klinefelter Syndrome

Classification according to ICD-10
N46	Male sterility
ICD-10 online (WHO version 2019)

As a pseudo-Klinefelter syndrome referred to the lack of or reduced endocrine activity of the testis with unusual formation or regression of primary or secondary sex characteristics as a result of sclerosis of the seminiferous tubules by the degeneration of the Leydig cells .

The cause is unknown and the karyotype of men with pseudo-Klinefelter syndrome is normal (46, XY).

The pseudo-Klinefelter syndrome manifests itself in the third to fourth decade of life with loss of libido and potency as well as the absence of sperm .

The clinical symptoms are similar to those of Klinefelter syndrome .

literature

• H. Niermann: Klinefelter and pseudo-Klinefelter syndrome. Observations on 30 cases. In: H. Nowakowski: Modern developments in the progestin area: Hormones in veterinary medicine . Springer Verlag 1960, pp. 365-375

Individual evidence

1. ↑ ^{a b c} Klinefelter syndrome . In: Susanne Andreae et all: Lexicon of diseases and examinations . Georg Thieme Verlag, Stuttgart / New York, 2nd edition 2008 (PDF). Retrieved May 17, 2018.
2. ↑ ^{a b} Klinefelter Syndrome , on medizin.de, October 4, 2017. Retrieved May 17, 2018.

This article is about a health issue. It is not used for self-diagnosis and does not replace a diagnosis by a doctor. Please note the information on health issues !