Bellini duct carcinoma

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Classification according to ICD-10
C64 Malignant neoplasm of the kidney, excluding the renal pelvis
ICD-10 online (WHO version 2019)

The Bellini duct carcinoma is a very rare form of renal cell carcinoma that originates in the collecting ducts (in Latin tubulus renalis colligens , Ductus Bellini ).

Synonyms are: multiple duct carcinoma; Collector tube carcinoma; DBK; Bellini duct carcinoma

The name refers to the Italian anatomist and kidney physiologist Lorenzo Bellini .

distribution

This form accounts for about 1% of all renal cell carcinomas. To date, several hundred people have been reported to be affected, and the age at disease ranged from 13 to 38 years. The male sex is affected about twice as often.

Clinical manifestations

The clinical appearance and diagnosis corresponds to that described under renal cell carcinoma . This type of tumor is considered to be particularly aggressive.

Differential diagnostics

Urothelial carcinomas of the upper urinary tract and papillary renal cell carcinomas are to be distinguished.

therapy

The treatment is performed surgically .

literature

  • MR Abern, M. Tsivian, TJ Polascik, CL Coogan: Characteristics and outcomes of tumors arising from the distal nephron. In: Urology. Volume 80, Number 1, July 2012, pp. 140-146, doi : 10.1016 / j.urology.2012.03.034 , PMID 22626576 .
  • PI Karakiewicz, QD Trinh, N. Rioux-Leclercq et al .: Collecting duct renal cell carcinoma: a matched analysis of 41 cases. In: European urology. Volume 52, number 4, October 2007, pp. 1140-1145, doi : 10.1016 / j.eururo.2007.01.070 , PMID 17336449 .
  • B. Li, Q. Ding: A case report of collecting duct carcinoma of the kidney coexistent with giant adrenal myelolipoma. In: Canadian Urological Association journal = Journal de l'Association des urologues du Canada. Volume 6, number 2, April 2012, pp. E97-100, doi : 10.5489 / cuaj.11087 , PMID 22511446 , PMC 3328585 (free full text).

Individual evidence

  1. ↑ a b Collective canal carcinoma. In: Orphanet (Rare Disease Database).
  2. ↑ a b c M. Parr: Immunohistochemical examination of the Bellini duct carcinoma to differentiate between urothelial carcinomas of the upper urinary tract and papillary renal cell carcinomas. Dissertation, 2014
  3. ^ S. Wolter, A. Heidenreich, B. Krug, U. Engelmann: Sarkomatoides Ductus-Bellini-Karzinom: a rare renal tumor. In: Current Urology. 31, 2000, p. 431, doi : 10.1055 / s-2000-9483 .
  4. ^ Anvil knowledge for physicians
  5. ↑ CG Hammerschmied, B. Walter, A. Hartmann: Renal cell carcinoma 2008. Histopathology, molecular genetics and new therapies. In: The Pathologist. Volume 29, Number 5, September 2008, pp. 354-363, doi : 10.1007 / s00292-008-1011-5 , PMID 18592242 .
  6. ↑ N. Tokuda, S. Naito, O. Matsuzaki, Y. Nagashima, S. Ozono, T. Igarashi: Collecting duct (Bellini duct) renal cell carcinoma: a nationwide survey in Japan. In: The Journal of urology. Volume 176, Number 1, July 2006, pp. 40-43, doi : 10.1016 / S0022-5347 (06) 00502-7 , PMID 16753362 .

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