Meyer's dysplasia
| Classification according to ICD-10 | |
|---|---|
| Q78.8 | Meyer's dysplasia |
| ICD-10 online (WHO version 2019) | |
The Meyersche dysplasia (according to J. Mayer, 1964) or dysplasia epiphysealis capitis femoris is questionable as mere unusually extending ossification Ossifikationsvariante , or as mild form a bone malformation ( dysplasia ) of the multiple epiphyseal dysplasia to look at.
It is limited exclusively to the femoral heads and is usually bilateral, and manifests itself as delayed and irregular ossification of the femoral heads during early childhood. The frequency peak is between two and five years. Since there are usually no complaints ( symptoms ) or movement abnormalities, in the majority of cases it is an incidental finding in an imaging for another reason. Boys are five times more likely to be affected than girls.
In terms of differential diagnosis, the distinction from M. Perthes is essential. Main distinguishing features are:
- Missing subchondral infraction line and missing condensation as typical for M. Perthes
- Blander course with normalization in the course. At most, a slight flattening of the epiphysis can remain
- No clinical complaints, no restriction of movement
- No signs of irritation on the hip joint, especially no joint effusion
Transitions to M. Perthes are described, however, so that follow-up checks are useful until normalization. There is no reliable knowledge about the cause ( etiology ).
swell
- W. Schuster, D. Färber (editor): Children's radiology. Imaging diagnostics. Springer 1996, ISBN 3-540-60224-0 .
- Willibald Pschyrembel : Clinical Dictionary , 266th, updated edition, de Gruyter, Berlin 2014, ISBN 978-3-11-033997-0 , keyword "Dysplasia epiphysealis capitis femoris"
Individual evidence
- ↑ J. MEYER: DYSPLASIA EPIPHYSEALIS CAPITIS FEMORIS. A CLINICAL-RADIOLOGICAL SYNDROME AND ITS RELATIONSHIP TO LEGG-CALV'E-PERTHES DISEASE. In: Acta orthopaedica Scandinavica. Volume 34, 1964, pp. 183-197, ISSN 0001-6470 . PMID 14165355 .
- ↑ O. Khermosh, p Wientroub: Dysplasia epiphysealis capital femoral. Meyer's dysplasia. In: The Journal of bone and joint surgery. British volume. Volume 73, Number 4, July 1991, pp. 621-625, ISSN 0301-620X . PMID 1906473
Web links
- Meyer's dysplasia. In: Orphanet (Rare Disease Database).
