Congenital subclavian steal sequence

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Classification according to ICD-10
Q25.8 Other congenital malformations of the great arteries
ICD-10 online (WHO version 2019)

The congenital subclavian steal sequence is a very rare congenital vascular malformation with an anomaly in the vascular outlet of a subclavian artery resulting in reduced blood flow to the arm on the same side.

Synonyms are: congenital subclavian steal syndrome; Subclavian tap syndrome, congenital; congenital pulmonary subclavian steal syndrome

The first description comes from 1963 by the Indian cardiologist Rashid A Massumi, an exact system was carried out in 1979 by BE Victoria and colleagues.

distribution

The frequency is not known; significantly fewer than 100 people have been reported to be affected.

Clinical manifestations

Clinical criteria are:

  • Reduced blood flow in one arm with a difference in blood pressure and pulse
  • In the arcus aortae dexter (aortic arch displaced to the right) usually the left-sided subclavian artery
  • Sound of flow over the affected artery
  • almost always congenital heart defects
  • only rarely neurological abnormalities

In addition, an auricle malformation or choanal atresia can occur.

Differential diagnosis

Other forms of subclavian steal syndrome are to be distinguished .:

literature

  • M. Ciftel, F. Kardelen, G. Akcurin, H. Ertug: Congenital subclavian steal syndrome associated with heterotaxy syndrome and atrioventricular septal defect. In: Pediatric cardiology. Volume 32, Number 8, December 2011, pp. 1249-1250, doi: 10.1007 / s00246-011-0048-z , PMID 21779966 .
  • AL Georgiadis: Congenital subclavian steal associated with atresia of a left innominate artery. In: Journal of vascular and interventional neurology. Volume 2, Number 2, April 2009, pp. 180-181, PMID 22518252 , PMC 3317339 (free full text).
  • N. Carano, P. Piazza, A. Agnetti, U. Squarcia: Congenital pulmonary steal phenomenon associated with tetralogy of Fallot, right aortic arch, and isolation of the left subclavian artery. In: Pediatric cardiology. Volume 18, Number 1, 1997 Jan-Feb, pp. 57-60, doi: 10.1007 / s002469900111 , PMID 8960496 .

Individual evidence

  1. ↑ a b c Bernfried Leiber (founder): The clinical syndromes. Syndromes, sequences and symptom complexes . Ed .: G. Burg, J. Kunze, D. Pongratz, PG Scheurlen, A. Schinzel, J. Spranger. 7., completely reworked. Edition. tape 2 : symptoms . Urban & Schwarzenberg, Munich et al. 1990, ISBN 3-541-01727-9 .
  2. ↑ a b A. T. Mamopoulos, B. Luther: Congenital subclavian steal syndrome with multiple cerebellar infarctions caused by an atypical circumflex retroesophageal right aortic arch with atretic aberrant left subclavian artery. In: Journal of Vascular Surgery . Volume 60, number 3, September 2014, pp. 776-779, doi: 10.1016 / j.jvs.2013.06.086 , PMID 23958067 .
  3. ↑ RA MAassumi: The Congenital Variety Of The "subclavian steal" syndrome. In: Circulation . Volume 28, December 1963, pp. 1149-1152, doi: 10.1161 / 01.cir.28.6.1149 , PMID 14082930 .
  4. ^ BE Victorica, LH Van Mierop, LP Elliott: Right aortic arch associated with contralateral congenital subclavian steal syndrome. In: The American journal of roentgenology, radium therapy, and nuclear medicine. Volume 108, Number 3, March 1970, pp. 582-590, doi: 10.2214 / ajr.108.3.582 , PMID 5415934 .
  5. ^ CJ Dainton, K. Iglar, V. Prabhudesai: A case of right-sided congenital subclavian steal. In: The Canadian journal of cardiology. Volume 26, number 1, January 2010, pp. E15 – e16, doi: 10.1016 / s0828-282x (10) 70335-4 , PMID 20101360 , PMC 2827228 (free full text).