Chondromatosis

Classification according to ICD-10
D48.0	Chondromatosis
ICD-10 online (WHO version 2019)

A Chondromatosis is a disease (of many to very many) which is the formation of multiple Chondromata (as ene or Ekchondrome comes) in the bone or in the joints.

From a osteochondromatosis is used when multiple Chondromata ossify and thus as osteochondroma or (in the case ossified Ekchondrome) as cartilaginous exostosis be called.

Independent clinical pictures are

• the synovial Chondromatosis even Gelenkchondromatose
• the generalized Enchondromatosis , also Enchondromatosis Spranger type VI ; an autosomal - recessive inherited disease
• the Maffucci syndrome , a rare, sporadic Enchondromatosis with hemangiomas and lymphangioma and increased risk of malignancy.
• the Ollier's disease , also Enchondromatosis-Ollier or unilateral multiple Chondromatosis
• the multiple osteochondromatosis , an autosomal dominant inherited disease , usually the metaphyses of the long bones on

Further clinical pictures mentioned in the literature are

• the Metachondromatosis ,
• the Spondyloenchondromatose even Spondyloenchondrodysplasie , Enchondromatosis with spondyloakraler dysplasia

Individual evidence

1. ↑ Alphabetical directory for ICD-10-WHO version 2019, volume 3. German Institute for Medical Documentation and Information (DIMDI), Cologne, 2019, p. 154

This article is about a health issue. It is not used for self-diagnosis and does not replace a diagnosis by a doctor. Please note the information on health issues !