Acute interstitial pneumonia
| Classification according to ICD-10 | |
|---|---|
| J84.1 | Other interstitial lung diseases with fibrosis Acute interstitial pneumonia (AIP) |
| ICD-10 online (WHO version 2019) | |
The acute interstitial pneumonitis (abbreviation AIP , earlier after internists Louis Hamman and the pathologist Arnold Rice Rich also Hamman-Rich syndrome named) is a usually fatal ( lethal ) running pneumonia (pneumonia). It is a clinical syndrome of unknown cause, also known as " idiopathic ARDS ". The disease progresses rapidly and leads to death from lung failure in about 80% of those affected within an average of six weeks.
Symptoms and diagnosis
The patients suffer from rapidly increasing breathlessness and cough, about 50% of them have a fever . The x-rays of the chest ( thorax ) show spotty, bilateral and usually symmetrically arranged condensation of the lungs, preferably in the lower, after prolonged lying in the posterior lung.
treatment
Treatment with glucocorticoids and cyclophosphamide is usually initiated, but their positive effect on the course of the disease is questionable and not proven.
history
The disease was first described in 1838 by Dominic John Corrigan (1802–1880), in 1897 by Georg Eduard Rindfleisch (1836–1908) as "cystic cirrhosis" and in 1915 by David Paul von Hansemann (1858–1920) as "reticular lymphangitis". After several joint publications by the Americans Louis Virgil Hamman and Arnold Rice Rich about the disease between 1933 and 1944, it was known for a long time as Hamman-Rich syndrome . The current term "acute interstitial pneumonia" has been favored since the 1990s.
Individual evidence
- ↑ a b c U. Costabel: The new classification of idiopathic interstitial pneumonia. In: Pneumologie , 54, 2000, pp. 447-453, PMID 11089397 , doi: 10.1055 / s-2000-7693 .
- ↑ whonamedit.com, accessed April 6, 2007.
