Hornstein-Knickenberg Syndrome

The Hornstein-Knickenberg syndrome (syn. Fibromatosis cutis) is a very rare syndrome . Characteristic are peri follicular fibroids of the trunk or head, pendulous fibroids in the area of the groin, armpits and neck as well as adenomatous colon polyps . The fibroids are treated surgically, the colon polyps require consistent check-ups.

The clinical picture was discovered and published in 1975 by a German dermatology professor in Erlangen ( Otto P. Hornstein ) and his assistant Monika Knickenberg. Several months later, however, the same disease was also described by Canadians Arthur R. Birt, Georgina R. Hogg and W. James Dubé. Hence the syndrome is also known as Birt-Hogg-Dubé syndrome .

Individual evidence

^ P. Altmeyer: Therapielexikon Dermatologie und Allergologie . Springer, 2005, p. 1086, ISBN 978-3-540-23781-5 , books.google.de
↑ P. Altmeyer et al .: Springer Encyclopedia Dermatology, Allergology, Environmental Medicine . Springer, 2002, pp. 529-30, ISBN 3-540-41361-8 , books.google.de
↑ Otto P. Hornstein, Monika Knickenberg: Perifollicular fibromatosis cutis with polyps of the colon - a cutaneo-intestinal syndrome sui generis . In: Archives for Dermatological Research . tape 253 , no. 2 , 1975, p. 161-175 , doi : 10.1007 / BF00582068 .
↑ Arthur R. Birt, Georgina R. Hogg, W. James Dube: Hereditary Multiple Fibrofolliculomas With Trichodiscomas and Acrochordons . In: Arch Dermatol . tape 113 , no. 12 , November 1, 1977, pp. 1674–1677 , doi : 10.1001 / archderm.1977.01640120042005 .

[1] P. Altmeyer: Therapielexikon Dermatologie und Allergologie . Springer, 2005, p. 1086, ISBN 978-3-540-23781-5 , books.google.de

[2] P. Altmeyer et al .: Springer Encyclopedia Dermatology, Allergology, Environmental Medicine . Springer, 2002, pp. 529-30, ISBN 3-540-41361-8 , books.google.de

[3] Otto P. Hornstein, Monika Knickenberg: Perifollicular fibromatosis cutis with polyps of the colon - a cutaneo-intestinal syndrome sui generis . In: Archives for Dermatological Research . tape 253 , no. 2 , 1975, p. 161-175 , doi : 10.1007 / BF00582068 .

[4] Arthur R. Birt, Georgina R. Hogg, W. James Dube: Hereditary Multiple Fibrofolliculomas With Trichodiscomas and Acrochordons . In: Arch Dermatol . tape 113 , no. 12 , November 1, 1977, pp. 1674–1677 , doi : 10.1001 / archderm.1977.01640120042005 .