Roviralta Syndrome

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Classification according to ICD-10
Q40.0 Congenital hypertrophic pyloric stenosisInfobox ICD
K44.9 Diaphragmatic hernia without entrapment and without gangrene
ICD-10 online (WHO version 2019)

The Roviralta syndrome (Phrenopylorisches syndrome) is a combination of hiatal hernia and pyloric stenosis .

The name refers to the author of the first description from 1946 by the Spanish pediatric surgeon Emilio Roviralta . (Quoted from Leiber)

distribution

The incidence is given as 5% for pyloric stenosis.

Clinical manifestations

Clinical criteria are:

  • Persistent vomiting, usually since birth
  • Evidence of blood in the stool, possibly anemia
  • Swallowing disorder
  • after a few weeks signs of pyloric stenosis

diagnosis

In the ultrasound examination evidence of pyloric stenosis and gastroesophageal reflux , in the esophageal swallow evidence of a hiatal hernia possibly with reflux esophagitis .

therapy

The hiatal hernia often recedes after an operation on the pyloric stenosis.

literature

  • Marcel Bettex (ed.), Max Grob (introductory), D. Berger (editing), N. Genton, M. Stockmann: Pediatric Surgery. Diagnostics, indication, therapy, prognosis. 2nd, revised edition, Thieme, Stuttgart / New York 1982,  ISBN 3-13-338102-4 , p. 7.34
  • WC Hecker: [Indication for operation and results in cardia insufficiency with or without hiatic hernia in childhood (author's transl)]. In: Monthly Pediatric: Organ of the German Society for Pediatrics. Vol. 130, No. 3, March 1982, pp. 122-125, PMID 7087968 .
  • E. Roviralta: [Association of hypertrophic stenosis of the pylorus and partial gastric ectopia (phreno-pyloric syndrome)]. In: Archives des maladies de l'appareil digestif et des maladies de la nutrition. Vol. 39, No. 11, November 1950, pp. 1103-1114, PMID 14800484 .

Individual evidence

  1. ↑ a b Bernfried Leiber (founder): The clinical syndromes. Syndromes, sequences and symptom complexes . Ed .: G. Burg, J. Kunze, D. Pongratz, PG Scheurlen, A. Schinzel, J. Spranger. 7., completely reworked. Edition. tape 2 : symptoms . Urban & Schwarzenberg, Munich et al. 1990, ISBN 3-541-01727-9 .
  2. ↑ a b W. Schuster, D. Färber (editor):  Children's radiology. Imaging diagnostics.  Springer 1996,  ISBN 3-540-60224-0 . Vol. II