Trigonocephaly

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With the term trigonocephaly ( ancient Greek τρίγωνος TRIGONOS , triangular ' κεφαλή kephale , head') is in the human medicine described a special head shape by a triangular skull shape ( triangle skull features) and in particular by a prominent, keel-like forehead strikes.

In people with a trigonocephalus, the development of the sutura frontalis ( metophical suture ) is unusually early . As a result of this ossification disorder, the skull has acquired a triangular-looking shape, with the forehead protruding and the tubera frontalia (ossification centers of the frontal bone ) missing, which can lead to the development of oxycephalus ( pointed skull ).

Trigonocephaly occurs partly as a symptom of a syndrome complex that is often caused by chromosomes . It occurs above average in people with partial trisomy 3p , the Patau syndrome (trisomy 13), the Edwards syndrome (trisomy 18), the Bohring-Opitz syndrome (C syndrome / Opitz-C trigonocephaly / Opitz- Trigonocephaly syndrome).

Due to the unusual shape of the head, the brain is forced to adapt accordingly. Whether and, if so, to what extent this leads to a reduction in the expected cognitive abilities of the respective person and whether a surgical intervention is necessary, varies greatly. The greatest dependence here is evidently in the type and severity of the other symptoms. This also explains why surgical correction of the head shape can only have a cosmetic effect.

literature

  • G. Neuhauser: The C-Trigonocephaly-Syndrome . In: Geistige Behavior , 38, 1999, issue 2, p. 196 f.
  • O. Röhrer-Ertl, K. Schneider, Chr. Becker-Gaab: On the teratological case history of trigonocephaly according to Welcker in prehistory . In: Contributions to archeozoology and prehistoric anthropology , Volume III. Konstanz 2001, pp. 194-195

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