Müller-Weiss syndrome

Classification according to ICD-10
M87.0	Bone necrosis, idiopathic aseptic
ICD-10 online (WHO version 2019)

The Muller-Weiss syndrome is a rare disease with bilateral osteochondrosis of the navicular bone in the adult.

Synonyms are: aseptic osteochondrosis or aseptic osteonecrosis, type Müller-Weiss.

The syndrome must be differentiated from Köhler's disease in children and adolescents.

The name refers to the authors of the first descriptions from 1927 by the German orthopedic surgeon Walther Müller (1888-1949) and the Viennese radiologist Konrad Weiss (1891-1976).

root cause

The etiology is unknown; (repeated) trauma may play a role.

Clinical manifestations

Clinical criteria are:

Shooting pain on both sides of the back of the foot when walking
Splayfoot , flat foot , hammer toe formation (secondary)
Onset of the disease in adulthood with a frequency peak between 40 and 60 years of age, occurring more frequently in women.

diagnosis

The x-ray shows a pronounced flattening of the navicular bone with an apparent displacement in the medial and dorsal direction. An early diagnosis is possible using magnetic resonance imaging .

pathology

A focal circulatory disorder leads to necrosis of the undersupplied bone section. After remodeling processes, the defect usually heals with deformation of the bone.

literature

RJ Bartolotta, JC McCullion, LM Belfi, KD Hentel: Mueller-Weiss syndrome: imaging and implications. In: Clinical imaging. [electronic publication before printing] June 2014, ISSN 1873-4499 . doi : 10.1016 / j.clinimag.2014.06.012 . PMID 25064253 .
B. Tosun, F. Al, A. Tosun: Spontaneous osteonecrosis of the tarsal navicular in an adult: Mueller-Weiss syndrome. In: The Journal of foot and ankle surgery: official publication of the American College of Foot and Ankle Surgeons. Vol. 50, No. 2, 2011 Mar-Apr, pp. 221-224, ISSN 1542-2224 . doi : 10.1053 / j.jfas.2010.10.019 . PMID 21354008 .
B. Reade, G. Atlas, J. Distazio, S. Kruljac: Mueller-Weiss syndrome: an uncommon cause of midfoot pain. In: The Journal of foot and ankle surgery: official publication of the American College of Foot and Ankle Surgeons. Vol. 37, No. 6, 1998 Nov-Dec, pp. 535-539, ISSN 1067-2516 . PMID 9879050 .

Individual evidence

↑ ^a ^b ^c Bernfried Leiber (founder): The clinical syndromes. Syndromes, sequences and symptom complexes . Ed .: G. Burg, J. Kunze, D. Pongratz, PG Scheurlen, A. Schinzel, J. Spranger. 7., completely reworked. Edition. tape 2 : symptoms . Urban & Schwarzenberg, Munich et al. 1990, ISBN 3-541-01727-9 .
↑ W. Müller: About a peculiar double-sided change in the navicular pedis in adults. In: Deutsche Zeitschrift für Chirurgie , Leipzig, 1927, Vol. 201, pp. 84–87.
↑ K. Weiss: About the “malacia” of the os naviculare pedis. In: Advances in the field of X-rays , 1927, Vol. 45, pp. 63-67.
↑ Where named it
^ SE De Marchi, SS Monteiro, E. d. Fernandes: Mueller Weiss syndrome – case report. In: Revista da Associação Médica Brasileira (1992). Vol. 60, No. 2, 2014 Mar-Apr, pp. 103-104, ISSN 0104-4230 . PMID 24918995 .
Jump up ↑ J. Haller, DJ Sartoris, D. Resnick, MN Pathria, D. Berthoty, B. Howard, D. Nordstrom: Spontaneous osteonecrosis of the tarsal navicular in adults: imaging findings. In: American Journal of Roentgenology . Vol. 151, No. 2, August 1988, pp. 355-358, ISSN 0361-803X . doi : 10.2214 / ajr.151.2.355 . PMID 3260727 .

[Leiber-1] Bernfried Leiber (founder): The clinical syndromes. Syndromes, sequences and symptom complexes . Ed .: G. Burg, J. Kunze, D. Pongratz, PG Scheurlen, A. Schinzel, J. Spranger. 7., completely reworked. Edition. tape 2 : symptoms . Urban & Schwarzenberg, Munich et al. 1990, ISBN 3-541-01727-9 .

[2] W. Müller: About a peculiar double-sided change in the navicular pedis in adults. In: Deutsche Zeitschrift für Chirurgie , Leipzig, 1927, Vol. 201, pp. 84–87.

[3] K. Weiss: About the “malacia” of the os naviculare pedis. In: Advances in the field of X-rays , 1927, Vol. 45, pp. 63-67.

[4] Where named it

[5] SE De Marchi, SS Monteiro, E. d. Fernandes: Mueller Weiss syndrome – case report. In: Revista da Associação Médica Brasileira (1992). Vol. 60, No. 2, 2014 Mar-Apr, pp. 103-104, ISSN 0104-4230 . PMID 24918995 .

[6] Jump up ↑ J. Haller, DJ Sartoris, D. Resnick, MN Pathria, D. Berthoty, B. Howard, D. Nordstrom: Spontaneous osteonecrosis of the tarsal navicular in adults: imaging findings. In: American Journal of Roentgenology . Vol. 151, No. 2, August 1988, pp. 355-358, ISSN 0361-803X . doi : 10.2214 / ajr.151.2.355 . PMID 3260727 .