Zuelzer-Kaplan syndrome
Classification according to ICD-10 | |
---|---|
D55.9 | Anemia due to enzyme defects, unspecified |
ICD-10 online (WHO version 2019) |
The Zuelzer-Kaplan syndrome , English Crosby's syndrome , is a rare congenital hemolytic anemia due to enzyme defects, hemoglobinopathies or defects in the cell membrane of the erythrocytes .
The names refer to the authors of descriptions from 1950 by the German - American hematologist and pediatrician Wolf William Zülzer and E. Kaplan . and the American hematologist William Holmes Crosby (1914-2005).
The names are no longer in use, instead different forms of congenital hemolytic anemia are distinguished.
The syndrome is not to be confused with Caplan syndrome , silicoarthritis, or Zuelzer-Wilson syndrome , a congenital aganglionosis .