Zuelzer-Kaplan syndrome

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Classification according to ICD-10
D55.9 Anemia due to enzyme defects, unspecified
ICD-10 online (WHO version 2019)

The Zuelzer-Kaplan syndrome , English Crosby's syndrome , is a rare congenital hemolytic anemia due to enzyme defects, hemoglobinopathies or defects in the cell membrane of the erythrocytes .

The names refer to the authors of descriptions from 1950 by the German - American hematologist and pediatrician Wolf William Zülzer and E. Kaplan . and the American hematologist William Holmes Crosby (1914-2005).

The names are no longer in use, instead different forms of congenital hemolytic anemia are distinguished.

The syndrome is not to be confused with Caplan syndrome , silicoarthritis, or Zuelzer-Wilson syndrome , a congenital aganglionosis .

Web links

Individual evidence

  1. ^ Who named it Crosby's syndrome
  2. E. Kaplan, WW Zuelzer: Familial nonspherocytic hemolytic anemia. In: Blood , New York, 1950, Vol. 5, No. 9, pp. 811-821.
  3. ^ WH Crosby: Hereditary non spherocytic hemolytic anemia. In: Blood , New York, 1950, Vol. 5, No. 3, pp. 233-253.