Heartctopia
| Classification according to ICD-10 | |
|---|---|
| Q24.8 | Ectopia cordis |
| ICD-10 online (WHO version 2019) | |
Heartctopia , ectocardia, cardiocele ( Greek Ectopia cordis ) is a rare congenital displacement ( ectopia ) of the heart from the chest. So far, only 210 cases have been documented.
In the case of defects in the chest wall , the fetal heart can be displaced in front of the chest ( ectocardia thoracica ) or in the case of larger gaps in the diaphragm ( diaphragm) in the abdominal cavity ( ectocardia subthoracica ).
diagnosis
Even Prenatal can ectopia cordis by sonography be detected (ultrasound). If ectopia cordis is suspected , a fetal echocardiography should be performed. Once the child is born, at least the thoracic ectocardia becomes characteristic: the heart is shifted in front of the chest and bulges outwards in a clearly visible manner . The skin at this point can either be normal or absent.
therapy
If a diagnosis is made during pregnancy, an interdisciplinary treatment plan should be drawn up before the birth so that optimal cooperation between pediatrics , neonatology , cardiac surgery , pediatric surgery and plastic surgery is guaranteed.
It is advisable to give birth by caesarean section ( Caesarean section ) to prevent contusion of the outwardly displaced heart during the birth.
The therapy consists of the surgical removal of the causes of the heart topia (gaps in the sternum, gaps in the diaphragm, etc.).
To protect the child until the operation, a plastic compression girdle is used to protect the heart from injuries and bumps.
forecast
The prognosis of heartctopia is poor. External compression of the ectopic heart often leads to life-threatening cardiac arrhythmias . The ectopia cordis can only be surgically corrected to a minor extent .
Web links
- Lee Shao-tsu: Ectopia cordis congenita. In: The Thoracic and Cardiovascular Surgeon. 5, 1957, p. 197, doi : 10.1055 / s-0028-1102556 .
- Michael Entezami: Sonographic malformation diagnostics. In: Lehratlas der fetal ultrasound examination , Thieme, p. 91 ( limited preview in the Google book search).
- Thomas W. Sadler, The embryological origin of ventral body wall defects . Seminar for Pediatric Surgery (19/3 pages 209–214), August 2010 doi: 10.1053 / j.sempedsurg.2010.03.006
- S. Pius, H. Abubakar Ibrahim, M. Bello, M. Bashir Tahir: Complete Ectopia Cordis: A Case Report and Literature Review. In: Case reports in pediatrics. Volume 2017, 2017, p. 1858621, doi : 10.1155 / 2017/1858621 , PMID 28503337 , PMC 5414485 (free full text).
- Spiegel-Online video report on a successful operation
- Spiegel-Online report
Individual evidence
- ↑ Lee Shao-tsu: Ectopia cordis congenita . In: Thoracic Surgery . tape 5 , no. 3 , November 1957, ISSN 0171-6425 , p. 197-212 , doi : 10.1055 / s-0028-1102556 .
- ↑ Simon Pius, Halima Abubakar Ibrahim, Mustapha Bello, Mohammed Bashir Tahir: Complete Ectopia Cordis: A Case Report and Literature Review . In: Case Reports in Pediatrics . tape 2017 , 2017, ISSN 2090-6803 , doi : 10.1155 / 2017/1858621 , PMID 28503337 , PMC 5414485 (free full text).
- ↑ a b Michael Entezami: Sonographic malformation diagnosis: teaching atlas of the fetal ultrasound examination; 7 tables . Georg Thieme Verlag, 2002, ISBN 978-3-13-129651-1 ( google.de [accessed on February 10, 2020]).