Pityriasis lichenoides et varioliformis acuta
| Classification according to ICD-10 | |
|---|---|
| L41.0 | Pityriasis lichenoides et varioliformis acuta [Mucha-Habermann] |
| ICD-10 online (WHO version 2019) | |
Pityriasis lichenoides et varioliformis acuta , abbreviation PLEVA , also called Mucha-Habermann disease , is a rarely occurring autoimmune disease that is not contagious. This is the more severe version of the Pityriasis lichenoides chronica .
Rash and lesion on the skin are characteristic of the disease . Even if the rash can be treated with the help of UV rays or the use of antibiotics or steroids , there is still no real cure for the disease. In most cases it disappears on its own after a while, but it can also go into remission , i.e. disappear for a while and then reappear. A chronic course in the form of pityriasis lichenoides chronica is also possible.
In pityriasis lichenoides et varioliformis acuta , the behavior of the T cells of the immune system is disrupted so that they are directed against the body . You thereby destroy your own cells in the skin, which leads to the rash.
The disease mostly occurs in childhood or in young adults, mostly males . It is common for the disease to be mistakenly diagnosed as chickenpox . A precise diagnosis of this disease is possible through a biopsy , i.e. by removing a small area of skin.
The cause of the disease has not yet been fully researched. A virus could be the trigger, but also vaccines or environmental factors such as B. a strong stress phase .
