Cystic adenomatoid malformation of the lungs

Classification according to ICD-10
Q33.8	Other congenital malformations of the lungs
ICD-10 online (WHO version 2019)

The Cystic adenomatoid malformation of the lung (CCAM abbreviation of English congenital cystic adenomatoid malformation ) is a lung malformation that to the group of hamartomas belongs.

Cystic adenomatoid malformation in a newborn on chest x-ray. You can see the large cystic changes in the left lung, which, due to their space-occupying effect, have led to a mediastinal shift to the right.

Cystic malformation on the CT image

to form

Types according to Stocker:

• Type I: (50%) One or more cysts with a diameter of 2–10 cm , in some cases also smaller cysts. Some of the cysts contain mucus.
• Type II: (40%) multiple small, uniform cysts 0.5–2 cm in diameter.
• Type III: (<10%) microscopic cysts. The imaging shows a solid mass.

Symptoms

Infections of the bronchi and lungs , shortness of breath , respiratory failure , heart failure and failure to thrive.

There is an association with pleuro-pulmonary blastoma .

Diagnosis

The CCAM can be seen prenatally on ultrasound . A close check after the diagnosis is made is necessary, as it can lead to rapid growth. However, 56% of the CCAMs discovered are regressing.

After the birth: X-ray of the lungs, CT , possibly bronchoscopy , NMR

therapy

If the death of the child is feared due to a strong increase in size before birth, an open prenatal removal of the process can be carried out in an appropriate center.

If the CCAM causes symptoms, surgical removal is recommended; asymptomatic cases are still controversial.

Web links

• Case presentation of a CCAM (with X-rays)

Individual evidence

1. ↑ BT Sweeney, KT Oldham: Pulmonary Malformations. In: P. Puri, M. Höllwarth: Pediatric Surgery. Springer, 2006, p. 107.
2. ↑ ^{a b c} Gerald Mandell: Imaging in Congenital Cystic Adenomatoid Malformation. In: Medscape.com. October 23, 2013, accessed December 26, 2014 . 
3. ↑ Guideline detail view. (No longer available online.) Association of Scientific Medical Societies in Germany. V. (AWMF), archived from the original on December 27, 2014 ; Retrieved December 26, 2014 (Guideline Pediatric Surgery on Lung Cysts). Info: The archive link was inserted automatically and has not yet been checked. Please check the original and archive link according to the instructions and then remove this notice.  
4. ↑ ^{a b} A. Strauss, MR Harrison, H. Hepp, B. Paek: Fetale Chirurgie. In: Speculum - Journal of Gynecology and Obstetrics. 19 (4), 2001, pp. 14-22.

This article is about a health issue. It is not used for self-diagnosis and does not replace a diagnosis by a doctor. Please note the information on health issues !