Koenen's tumor

Classification according to ICD-10
Q85.1	Tuberous (brain) sclerosis Bourneville (Pringle) Syndrome Epiloia
ICD-10 online (WHO version 2019)

A Koenen tumor on the toes.

A Koenen tumor (pronounced Ku: nen tumor), also called periungual fibroma (periungual = 'around the nail ') or subungual fibroma (subungual = 'under the nail'), is a benign mesenchymal tumor (a fibroma ) that occurs in the area of ​​the toenails or toenails.

description

Koenen tumors are a symptom of tuberous sclerosis (also called Pringle's disease), an autosomal - dominant hereditary disease . The benign tumors are skin-colored nodules that form in the area of ​​the toenails or toenails or below the nails and are typically 3 to 7 mm in size.

therapy

Koenen tumors can be surgically removed using excision or a CO ₂ laser .

Naming

The Koenen tumor is named after the Dutch neurologist Joannes Henricus Maria Koenen , who first photographed it in an article in 1932. It was first described in 1903 by the Munich doctor Richard Kothe .

Web links

• Koenen Tumor - definition and pictures on the website of the German Dermatological Society

further reading

• A. Dacunha: Images in clinical medicine. Periungual fibromas. In: The New England Journal of Medicine . Volume 359, Number 13, September 2008, p. 1381, ISSN  1533-4406 . doi : 10.1056 / NEJMicm073405 . PMID 18815399 .
• PE Ward, DJ McCarthy: Periungual fibroma. In: Cutis . Volume 46, Number 2, August 1990, pp. 118-124, ISSN  0011-4162 . PMID 2209075 .
• T. Kojima, T. Nagano, M. Uchida: Periungual fibroma. In: The Journal of hand surgery. Volume 12, Number 3, May 1987, pp. 465-470, ISSN  0363-5023 . PMID 3584898 .

Individual evidence

1. ^ ^{A b} P. Altmeyer: Koenen tumor. In: Encyclopedia of Dermatology, Venereology, Allergology, Environmental Medicine Springer-Verlag Berlin Heidelberg, 2008, ISBN 3-540-41361-8
2. ^ AL Berlin, RC Billick: Use of CO2 laser in the treatment of periungual fibromas associated with tuberous sclerosis. In: Dermatologic Surgery . Volume 28, Number 5, May 2002, pp. 434-436, ISSN  1076-0512 . PMID 12030880 .
3. ↑ J. Koenen: A familial hereditary form of tuberous sclerosis. In: Acta Psychiat. Volume 1, 1932, pp. 813-821.
4. ↑ R. Kothe: To the doctrine of the sebum gland tumors. In: Archives of Dermatology and Syphilology . Volume 68, 1903, pp. 273-278.
5. ↑ S. Borelli: Koenen, Kothe and the periungual fibroids in tuberous sclerosis. In: The dermatologist . Volume 50, Number 5, 1999, pp. 368-369. PMID 10412636 . doi : 10.1007 / s001050050923