Lichen planus moniliformis

Classification according to ICD-10
L44.0	Lichen planus moniliformis
ICD-10 online (WHO version 2019)

The Lichen ruber moniliformis is a rare chronic inflammatory skin disease with a strong itchy papules , hyperkeratosis and skin defects ( excoriation ).

Synonyms are: lichenoid trikeratosis; Kaposi-Bureau-Barrière-Grupper Syndrome; Latin keratosis lichenoides chronica; Lichen verrucosus et reticularis; Porokeratosis striata ; English Wise-Rein disease

The first description and name was given in 1886 by Moriz Kaposi .

The other names refer to descriptions from 1936 by the American dermatologist Fred Wise together with Charles R. Rein.

Spread and cause

The disease occurs more often around the age of 20 and then again around the age of 50, but can already occur in children. Men get sick more often than women.

The cause is not known. It could be a variant of lichen planus or hyperkeratosis follicularis et parafollicularis in cutem penetrans (Kyrle's disease).

Clinical manifestations

Clinical criteria are:

Hyperkeratotic, red-brown, strongly itchy papules confluent over a large area
Spread from one localization, mostly to the trunk and extensor sides of the extremities
Facial involvement as in seborrheic eczema or rosacea
possible involvement of the oral mucosa, larynx and eyes, as well as changes in the nails

Differential diagnosis

The following are to be distinguished:

literature

AW Li, W. Damsky, BA King: Keratosis lichenoides chronica successfully treated with isotretinoin and methotrexate. In: JAAD case reports. Vol. 3, No. 3, May 2017, pp. 205–207, doi: 10.1016 / j.jdcr.2017.02.009 , PMID 28443310 , PMC 5394184 (free full text).
A. Barisani, F. Savoia, P. Sgubbi, M. Negosanti, SD Infusino, E. Varotti, B. Passarini, A. Patrizi: Keratosis lichenoides chronica with atypical clinical presentation and variable histopathological features. In: Journal of the German Dermatological Society = Journal of the German Society of Dermatology: JDDG. Vol. 14, No. 11, November 2016, pp. 1139–1142, doi : 10.1111 / ddg.12950_g , PMID 27879072 .
F. Pistoni, A. Peroni, C. Colato, D. Schena, G. Girolomoni: Keratosis lichenoides chronica: Case-based review of treatment options. In: The Journal of dermatological treatment. Vol. 27, No. 4, August 2016, pp. 383-388, doi: 10.3109 / 09546634.2015.1115818 , PMID 26652284 (Review).

Individual evidence

↑ ^a ^b ^c ^d Encyclopedia Dermatology
↑ M. Kaposi: Lichen planus moniliformis. In: Quarterly Journal for Dermatology and Syphilis (Vienna) , Vol. 13, 1886, ſ. 571-582
^ F. Wise, CR Rein: Lichen planus moniliformis (morbus moniliformis lichenoides). Report of a case and description of a hitherto unrecorded histologic structure. In: Archives of Dermatology and Syphilology (Chicago) Vol. 34, 1936, p. 830-849
↑ S. Dogan, E. Kılınç, GE Özaygen, N. Atakan, .. Gököz, SE E: Childhood-Onset Keratosis Lichenoides Chronica Accompanied by Severe Hair Loss. In: Skinmed. Vol. 15, No. 3, 2017, pp. 211-213, PMID 28705285 .

[Altmeyer-1] Encyclopedia Dermatology

[2] M. Kaposi: Lichen planus moniliformis. In: Quarterly Journal for Dermatology and Syphilis (Vienna) , Vol. 13, 1886, ſ. 571-582

[3] F. Wise, CR Rein: Lichen planus moniliformis (morbus moniliformis lichenoides). Report of a case and description of a hitherto unrecorded histologic structure. In: Archives of Dermatology and Syphilology (Chicago) Vol. 34, 1936, p. 830-849

[4] S. Dogan, E. Kılınç, GE Özaygen, N. Atakan, .. Gököz, SE E: Childhood-Onset Keratosis Lichenoides Chronica Accompanied by Severe Hair Loss. In: Skinmed. Vol. 15, No. 3, 2017, pp. 211-213, PMID 28705285 .