Swyer-James Syndrome
| Classification according to ICD-10 | |
|---|---|
| J43.0 | McLeod syndrome |
| ICD-10 online (WHO version 2019) | |
The Swyer-James syndrome ( synonyms : SJS; Swyer-James-Macleod syndrome, SJMS; syndrome of the unilaterally light lung ) is the syndrome of the unilaterally hypertransparent (more radiolucent ) lung in the X-ray image .
The name designation refers to the authors of the first description in 1953 by the Canadian doctor Paul Robert Swyer and US radiologists GCW James in 1953 and a year later by the British Lung Doctor William Mathiseon Macleod.
Swyer-James syndrome is a rare variant of post-infectious bronchiolitis obliterans. It is one of the chronic obstructive airways diseases .
This leads to a hypoplasia of the lungs including their vascular architecture in early childhood. The cause is assumed to be pneumonia in early childhood . SJMS is an incurable disease of the respiratory tract with impaired lung function.
With the same name in the International Classification ICD-10 , the syndrome should not be confused with McLeod syndrome .
Clinical appearance
The symptoms are similar to those of chronic obstructive bronchitis or cystic fibrosis with recurrent infections , sputum and exertional dyspnea .
The disease begins as obliterative bronchiolitis with accompanying vasculitis , often after infections with adenovirus , measles, or pertussis .
Diagnosis
Conventional radiographs ( chest x-ray ) show the unilaterally increased radiation transparency and vascular poorness on the affected side. Further criteria are shifting of the heart to the healthy side, reduced mobility of the diaphragm on the affected side and bronchiectasis .
The findings can also be demonstrated in sectional image diagnostics such as MRI or CT .
literature
- W. Schuster, D. Färber: Pediatric radiology: imaging diagnostics . 2nd edition 1996, Springer, ISBN 3-540-15944-4
- D. Machado, F. Lima, C. Marques, R. Monteiro: Swyer-James-Macleod syndrome as a rare cause of unilateral hyperlucentment lung: Three case reports. In: Medicine. Volume 98, number 6, February 2019, p. E14269, doi: 10.1097 / MD.0000000000014269 , PMID 30732141 , PMC 6380820 (free full text).
- S. Hamada, M. Tsukino: Swyer-James-Macleod Syndrome: The Differential Diagnosis of Unilateral Hyperlucency. In: Internal medicine. Volume 57, number 17, 09 2018, pp. 2591-2592, doi: 10.2169 / internalmedicine.0725-17 , PMID 29709951 , PMC 6172534 (free full text).
Individual evidence
- ↑ Maximilian Reiser, Fritz-Peter Kuhn, Jürgen Debus: Dual series of radiology . 3. Edition. Georg Thieme Verlag, p. 180 f .
- ↑ emedicine
- ↑ a b Bernfried Leiber (founder): The clinical syndromes. Syndromes, sequences and symptom complexes . Ed .: G. Burg, J. Kunze, D. Pongratz, PG Scheurlen, A. Schinzel, J. Spranger. 7., completely reworked. Edition. tape 2 : symptoms . Urban & Schwarzenberg, Munich et al. 1990, ISBN 3-541-01727-9 .
- ^ PR Swyer, GC James: A case of unilateral pulmonary emphysema. In: Thorax. Volume 8, Number 2, June 1953, pp. 133-136, doi: 10.1136 / thx.8.2.133 , PMID 13077508 , PMC 1019253 (free full text).
- ↑ World Cup MacLeod: Abnormal transradiancy of one lung. In: Thorax. Volume 9, Number 2, June 1954, pp. 147-153, doi: 10.1136 / thx.9.2.147 , PMID 13179127 , PMC 1019360 (free full text).
- ↑ A Fertl, K Häußinger, MacLeod-Swyer-James Syndrome - a rare cause of a chronic obstructive airway disease, Pneumology 2009; 63 - P15 doi: 10.1055 / s-0029-1214021
- ↑ O. Tutar, DE Tekcan u. a .: Adult diagnosis of Swyer-James-Macleod syndrome. In: BMJ Case Reports. Volume 2012, 2012, S., ISSN 1757-790X . doi: 10.1136 / bcr-2012-007349 . PMID 23230247 .
- ↑ CF Erkasar, CE Caglar u. a .: Bilateral Swyer-James (Macleod's) syndrome. In: Indian journal of pediatrics. Volume 69, Number 5, May 2002, pp. 433-435, ISSN 0019-5456 . PMID 12061679 .
