Uterus didelphys

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Classification according to ICD-10
Q51.1 Uterus duplex with uterus bicollis and vagina duplex
Q51.2 Other forms of the uterus duplex
ICD-10 online (WHO version 2019)

The uterus didelphys (from ancient Greek δίς, δί dis, di "two" and δελφύς delphys "womb") is a congenital uterine malformation with a double system of the uterus and the vagina .

Synonyms are: bicornuate uterus, bicervical; Uterus duplex, uterus duplex bicollis

pathology

It is a complete duplication of the uterus including a double cervix and often a duplication of the vagina due to a disruption in embryonic development in which the lower parts of the Müller ducts have not merged .

distribution

The uterus didelphys accounts for about 8% of all anomalies in Müller's duct. The prevalence is around 0.5%.

Clinical manifestations

Clinical criteria are:

  • Double arrangement of the corpus and cervix uteri
  • mostly symptom-free, occasionally dyspareunia due to the vaginal septum (in 75%)
  • increased risk of positional anomalies in the unborn child and premature births during pregnancy

There is an association with renal agenesis and transverse vaginal septa with possible obstruction of a horn and unilateral hydrocolpos or hematocolpos .

diagnosis

Uterus didelphys on ultrasound

The diagnosis is usually made by sonography .

Differential diagnosis

Other uterine malformations such as uterus bicornis and uterus septus must be differentiated .

In the context of syndromes

This malformation can also occur in the OHVIRA syndrome (uterus didelphys with obstructed hemivagina and ipsilateral renal agenesis).

literature

  • HP Haiges, F. Huebner, RA Schuhmann: Gemini pregnancy in uterus didelphys. In: Obstetrics and gynecology. Volume 51, No. 5, May 1991, pp. 404-405, doi: 10.1055 / s-2007-1026168 , PMID 1869013 .
  • TC Park, HJ Lee: Pregnancy coexisting with uterus didelphys with a blind hemivagina complicated by pyocolpos due to Pediococcus infection: a case report and review of the published reports. In: The journal of obstetrics and gynecology research. Volume 39, No. 7, July 2013, pp. 1276-1279, doi: 10.1111 / jog.12049 , PMID 23718909 (review).
  • LM Cipullo, S. Milosavljevic, ED van Oudgaarden: Uterus didelphys: report of a puerperal torsion and a review of the literature. In: Case reports in obstetrics and gynecology , 2012, S. 190167, doi: 10.1155 / 2012/190167 , PMID 22919522 , PMC 3419394 (free full text).

Web links

Individual evidence

  1. ↑ Didelphys uterus. In: Orphanet (Rare Disease Database).
  2. ↑ a b c d Radiopaedia
  3. ↑ Entry on uterus didelphys in Flexikon , a Wiki of the DocCheck company
  4. ↑ Doubling of the uterus - hemivagina - renal agenesis. In: Orphanet (Rare Disease Database).