Hydrops fetalis
Classification according to ICD-10 | |
---|---|
P56 | Hydrops fetalis due to hemolytic disease |
P83.2 | Hydrops fetalis, not due to hemolytic disease |
ICD-10 online (WHO version 2019) |
As hydrops fetalis (Syn. Hydrops congenitus universalis ) in which is prenatal diagnosis a generalized fluid accumulation designated extending over large parts of the body of an unborn child has spread and in serous body cavities ( pleural , peritoneal cavity , pericardium is) as well as in the soft tissues. In the ultrasound , a pronounced edema is particularly visible, through which the child's skin is clearly lifted from the body.
A distinction is made between hydrops fetalis with and without isoimmunization (immunological and nonimmunological hydrops fetalis).
The presence of hydrops fetalis is considered a sonographic soft marker , which is an indication of a chromosome peculiarity , an organic malformation or a disease in the child.
It occurs more than average in:
- fetal anemia ( anemia in the unborn child), often due to a rhesus incompatibility or a parvovirus B19 infection ( rubella ) in the expectant mother , the full picture here is mostly characterized by ascites , pleural effusions and polyhydramnios . A spontaneous miscarriage can occur.
- Heart defects , especially coarctation of the aorta (narrowing of the transition between the aortic arch and thoracic aorta )
- Malformations of the lungs
- Twin pregnancies as an expression of a fetofetal transfusion syndrome
- Chylothorax
- Turner Syndrome (Monosomy X)
- Noonan syndrome (Turner-like syndrome)
- Edwards syndrome (trisomy 18)
- Multiple pterygium syndrome
- Fryns Syndrome
- less often Down syndrome (trisomy 21)
- various metabolic diseases
- Denys-Drash Syndrome
- Malformations of the urogenital tract
- Mevalonate kinase defect (very rare)
See also
Hemolytic disease of the newborn - nuchal translucency - hygroma colli - Dorsonuchales edema - hygroma dura mater - hygroma praepatellare - Hygromatosis
Web links
- Mevalonate kinase defect: an extremely rare differential diagnosis of hydrops fetalis doi : 10.1055 / s-2005-871506 (currently unavailable)
- Hydrops fetalis - On the pathology of a special form of dropsy with special consideration of case studies and clinical findings (2001)
Individual evidence
- ↑ Peter Reuter: Springer Lexicon Medicine. Springer, Berlin a. a. 2004, ISBN 3-540-20412-1 , p. 961.