Cystathionine
| Structural formula | |||||||||||||||||||
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| General | |||||||||||||||||||
| Surname | Cystathionine | ||||||||||||||||||
| other names |
( R ) - S - (2-Amino-2-carboxyethyl) - L -homocysteine |
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| Molecular formula | C 7 H 14 N 2 O 4 S | ||||||||||||||||||
| Brief description |
white solid |
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| properties | |||||||||||||||||||
| Molar mass | 222.26 g mol −1 | ||||||||||||||||||
| Physical state |
firmly |
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| Melting point |
> 300 ° C |
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| As far as possible and customary, SI units are used. Unless otherwise noted, the data given apply to standard conditions . | |||||||||||||||||||
Cystathionine is a non-proteinogenic amino acid that occurs in the biosynthesis of cysteine . Cystathionine is generated from homocysteine and serine by cystathionine-β-synthase . Due to the cystathionine γ-lyase , cystathionine can be hydrolyzed to yield cysteine and α-ketobutyrate formed.
Cystathionine is an amino acid with 2 stereocenters .
As Cystathioninurie which is an autosomal recessive hereditary disease described, in which there is accumulation of cystathionine, which via the urine is excreted.
Individual evidence
- ↑ a b c d e data sheet L-Cystathionine, ≥98% (TLC) from Sigma-Aldrich , accessed on January 24, 2020 ( PDF ).
- ↑ Entry on cysteine in Flexikon , a wiki of the DocCheck company , accessed on January 23, 2020.
- ↑ Cystathioninuria. In: Spectrum Lexicon Nutrition. Retrieved January 23, 2020 .