List of diseases of the skin and subcutaneous tissue according to ICD-10

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The International Statistical Classification of Diseases and Allied Health Problems (ICD-10) classifies skin and subcutaneous diseases in Chapter XII according to the key below.

L00 – L08 Skin and subcutaneous infections

code description Names of diseases (synonyms) Review article
L00 Staphylococcal scalded skin syndrome Staphylococcal scalded skin syndrome ( dermatitis exfoliativa neonatorum , pemphigus acutus neonatorum ) -
L01 impetigo Impetigo contagiosa , superficial folliculitis , impetiginization Impetigo contagiosa
L02 Skin abscess, boils and carbuncles Abscess , boils ( furunculosis ), carbuncles ( abscess ) -
L03 Phlegmon Cellulitis , acute lymphangitis , nail infection ( onychia , paronychia , perionyxis ) Gesichtsphlegmone , Omphalitis , cellulitis Phlegmon
L04 Acute lymphadenitis Acute lymphadenitis , lymph node abscess Lymphadenitis
L05 Pilonidal cyst Pilonidalzyste ( pilonidal sinus , Pilonidalsinus , coccygeal , coccyx cyst ) -
L06
L07
not forgiven - -
L08 Other local skin and subcutaneous infections Pyoderma , dermatitis purulent , dermatitis septic , dermatitis suppurative , Erythrasma -

L10-L14 Bullous dermatoses

code description Names of diseases (synonyms) Review article
L10 Pemphigus diseases Pemphigus vulgaris , pemphigus vegetans , pemphigus foliaceus , Brazilian pemphigus ( Fogo selvagem ), pemphigus erythematosus , senear usher syndrome , drug -induced pemphigus Pemphigus
L11 Other acantholytic dermatoses Acquired Keratosis Follicularis , Transient Acantholytic Dermatosis ( Transient Acantholytic Dermatosis Grover ) Acantholysis
L12 Pemphigoid diseases Bullous pemphigoid , Benign pemphigoid , Benign mucous membrane , chronic bullous dermatosis of childhood , acquired epidermolysis bullosa , Linear IgA bullous dermatosis Pemphigoid
L13 Other bullous dermatoses Dermatitis herpetiformis ( Dermatitis herpetiformis Duhring ), pustulosis subcornealis ( pustulosis subcornealis Sneddon-Wilkinson ) -
L14 * Bullous dermatoses in diseases classified elsewhere - -

L20-L30 dermatitis and eczema

code description Names of diseases (synonyms) Review article
L20 Atopic (endogenous) eczema Atopic dermatitis ( endogenous eczema , allergic eczema , Intrinsic eczema , Endogenous milk crust , neurodermatitis , atopic dermatitis atopica , Neurodermitis diffusa ), prurigo Besnier Atopic eczema , cradle cap
L21 Seborrheic eczema Seborrheic eczema , seborrhea capitis , seborrheic cradle cap , children's seborrheic eczema
L22 Diaper rash Diaper rash , Psoriasiform diaper rash , diaper rash , Windelerythem Contact dermatitis
L23 Allergic contact dermatitis Allergic contact dermatitis ( allergic contact eczema ), nickel allergy
L24 Toxic contact dermatitis Irritant contact dermatitis ( Non-allergic contact dermatitis , Irritant Contact Dermatitis , Irritant contact dermatitis ), acne venenata ( Kontaktakne ), chloracne , oil acne
L25 Unspecified contact dermatitis Baker's scabies
L26 Exfoliative dermatitis Exfoliative dermatitis , Pityriasis rubra ( Pityriasis rubra Hebra ) -
L27 Dermatitis due to orally, enterally or parenterally ingested substances - -
L28 Lichen simplex chronicus and prurigo Lichen simplex chronicus (Lichen Vidal), Neurodermitis chronica circumscripta , Prurigo nodularis , Prurigo , Prurigo Hebra , Prurigo mitis , Urticaria papulosa -
L29 Pruritus Pruritus ani , pruritus scrotalis , pruritus vulvae , pruritus anogenitalis Pruritus
L30 Other dermatitis Nummular Eczema , Dyshidrosis ( Pompholyx ), Candida Mykid ( Levurid ), Dermatophytid , Eczematid , Eczematoid Dermatitis , Infectious Dermatitis , Superinfected Eczema , Intertriginous Eczema , Pityriasis alba faciei Dermatitis ( eczema )

L40 – L45 Papulosquamous skin diseases

code description Names of diseases (synonyms) Review article
L40 psoriasis Psoriasis vulgaris , psoriasis nummular , pustular psoriasis Generalized , impetigo herpetiformis , psoriasis pustulosa Zumbusch , Acrodermatitis continua suppurativa ( Acrodermatitis continua suppurativa Hallopeau ), pustulosis palmaris et plantaris , guttate psoriasis , psoriatic arthritis , psoriasis inversa psoriasis
L41 Parapsoriasis Pityriasis lichenoides et varioliformis acuta ( Pityriasis lichenoides et varioliformis acuta Mucha-Habermann ), parapsoriasis guttata , papulosis lymphomatoides , small speckled parapsoriasis en plaques , large speckled parapsoriasis en plaques , parapsoriasis with poikiloderma Parapsoriasis
L42 Pityriasis rosea Pityriasis rosea ( rose lichen ) -
L43 Lichen planus Lichen planus hypertrophicus , lichen planus pemphigoides , lichenoid drug reaction , subacute lichen planus , lichen planus tropicus Lichen planus
L44 Other papulosquamous skin diseases Pityriasis rubra pilaris , lichen nitidus , lichen striatus , lichen planus moniliformis , infantile papular acrodermatitis ( Gianotti-Crosti syndrome ) -
L45 * Papulosquamous Skin Diseases in Diseases Classified Elsewhere - -

L50 – L54 urticaria and erythema

code description Names of diseases (synonyms) Review article
L50 Urticaria Allergic urticaria , idiopathic urticaria , cold urticaria , warm urticaria , urticaria factitia , urticarial dermographism , urticaria mechanica , cholinergic urticaria , contact urticaria , chronic urticaria , recurrent urticaria , periodic urticaria Urticaria
L51 Erythema exudativum multiforme Non-bullous erythema exudativum multiforme ( Erythema exudativum multiforme minus ), Bullous erythema exudativum multiforme ( Erythema exudativum multiforme majus , Stevens-Johnson syndrome ), Toxic epidermal necrolysis ( Lyell's syndrome ) Erythema exudativum multiforme
L52 Erythema nodosum Erythema nodosum -
L53 Other erythematous diseases Erythema toxicum , erythema annulare centrifugum , erythema marginatum , figured chronic erythema , erythroderma Erythema
L54 * Erythema in Diseases Classified Elsewhere Erythema marginatum in acute rheumatic fever

L55 – L59 Diseases of the skin and subcutaneous tissue caused by radiation

code description Names of diseases (synonyms) Review article
L55 Acute solar dermatitis Dermatitis solaris acuta ( sunburn ) -
L56 Other acute skin changes caused by ultraviolet rays Phototoxic reaction to drugs, photoallergic reaction to drugs Phototoxic contact dermatitis , Berloque dermatitis , urticaria solaris , polymorphic light eruption -
L57 Skin changes due to chronic exposure to non-ionizing radiation Actinic keratosis , ( keratosis senilis , keratosis solaris ), Actinic Reticuloid , Cutis rhomboidalis nuchae , Poikilodermia reticularis ( Poikilodermia Civatte reticularis ), cutis laxa senilis ( senile, actinic elastosis , elastosis senilis ), Strahlengranulom , Landmann skin , Seemann skin -
L58 Radiodermatitis acute radiodermatitis , chronic radiodermatitis Radiodermatitis
L59 Other diseases of the skin and subcutaneous tissue caused by radiation Erythema ab igne , chronic heat damage -

L60 – L75 Diseases of the skin appendages

code description Names of diseases (synonyms) Review article
L60 Diseases of the nails Unguis incarnatus ( ingrown nail ), onycholysis , onychogryposis ( onychogryphosis ), nail dystrophy , Beau-Reil transverse furrows , yellow nail syndrome ( yellow nail syndrome ) -
L61 not forgiven - -
L62 * Diseases of the nails in diseases classified elsewhere - -
L63 Alopecia areata Alopecia cranialis totalis ( alopecia totalis ), alopecia universalis , ophiasis Alopecia areata
L64 Androgenetic alopecia Male type alopecia , drug-induced androgenetic alopecia Androgenetic alopecia
L65 Other hair loss without scarring Telogen effluvium , anagen effluvium , Alopecia mucinosa Pinkus ( Alopecia mucinosa ) -
L66 Scarring alopecia (hair loss with scarring) Pseudopelade Brocq , Lichen planopilaris, lichen ruber follicularis , folliculitis decalvans , folliculitis et Perifolliculitis capitis abscedens et suffodiens Hoffmann ( Folliculitis et Perifolliculitis capitis abscedens et suffodiens ) Atrophodermia vermiculata , folliculitis ulerythematosa reticulata , Ulerythema acneiforme Scarring alopecia ( hair loss with scarring )
L67 Hair color and hair shaft abnormalities Trichorrhexis nodosa , canities , premature graying , heterochromia of the hair , poliosis , acquired poliosis circumscripta , fragilitas crinium -
L68 Hypertrichosis Increased hair growth , hirsutism , hypertrichosis lanuginosa acquisita , localized hypertrichosis , polytrichia Hypertrichosis
L69 not forgiven - -
L70 acne Acne vulgaris , Acne conglobata , Acne varioliformis , Acne necroticans miliaris , Acne tropica , Acne infantum , Acne excoriée des jeunes filles acne
L71 Rosacea Perioral dermatitis , rhinophyma Rosacea
L72 Follicular cysts of the skin and subcutaneous tissue Epidermal cyst , trichilemmal cyst , atheroma , pilar cyst , steatocystoma multiplex Follicular cyst
L73 Other diseases of the hair follicles Acnekeloid ( folliculitis sclerotisans nuchae ), pseudofolliculitis barbae , hidradenitis suppurativa , folliculitis barbae -
L74 Diseases of the eccrine sweat glands Miliaria rubra , Miliaria cristallina , Miliaria profunda , Miliaria tropica , Anhidrosis , Hypohidrosis Miliaria
L75 Diseases of the apocrine sweat glands Bromhidrosis , Chromhidrosis , Apocrine Miliaria , Fox-Fordyce Disease

L80 – L99 Other skin and subcutaneous diseases

code description Names of diseases (synonyms) Review article
L80 Vitiligo Vitiligo -
L81 Other skin pigmentation disorders Post-inflammatory hyperpigmentation , chloasma ( melasma ), ephelids ( freckles ), café-au-lait spots , lentigo , leukoderm , pigment purple , angioma serpiginosum , essential telangiectasia , tattoos -
L82 Seborrheic keratosis Seborrheic keratosis , dermatosis papulosa nigra , Leser-Trélat syndrome -
L83 Acanthosis nigricans Acanthosis nigricans , Papillomatosis confluens et reticularis ( Papillomatosis confluens et reticularis Gougerot-Carteaud ) -
L84 Corns and horns (skin) calluses Corns , calluses , callus , clavus -
L85 Other epidermal thickening Acquired ichthyosis , acquired keratosis palmoplantaris ( acquired keratoma palmoplantare ), keratosis punctata ( keratosis palmoplantaris ), xerosis cutis (xeroderma), cornu cutaneum , epidermal thickening -
L86 * Keratoma in Diseases Classified Elsewhere - -
L87 Disorders of transepidermal elimination Hyperkeratosis follicularis et parafollicularis in cutem penetrans ( Hyperkeratosis follicularis et parafollicularis in cutem penetrans Kyrle , Hyperkeratosis follicularis penetrans ), reactive perforating collagenosis , elastosis perforans serpiginosa -
L88 Pyoderma gangrenosum Pyoderma gangrenosum , ulcerative dermatitis , phageenic pyoderma -
L89 Decubitus ulcer Bedsores , pressure sores , ulcers -
L90 Atrophic skin diseases Lichen sclerosus et atrophicus , anetodermia , atrophodermia idiopathica , akrodermatitis chronica atrophicans Herxheimer , scars and fibroses of the skin, striae cutis atrophicae Skin atrophy
L91 Hypertrophic skin diseases Hypertrophic scar , keloid scar -
L92 Granulomatous diseases of the skin and subcutaneous tissue Granuloma annulare ( Granuloma annulare perforans ), necrobiosis lipoidica , granuloma faciale , ( Granuloma eosinophilicum faciei ), foreign body granuloma -
L93 Lupus erythematosus Discoid lupus erythematosus , subacute lupus cutaneous erythematosus , lupus erythematosus profundus , lupus panniculitis Lupus erythematosus
L94 Other localized connective tissue diseases Scleroderma circumscribed ( morphea , Localized scleroderma ), Linear scleroderma ( Tape-like scleroderma , scleroderma en coup de saber ), calcinosis cutis , Sclerodactyly , Gottron papules , Poikilodermia atrophic vascularis ( Poikilodermia atrophic vascularis Jacobi ), Ainhum Scleroderma
L95 Vasculitis not elsewhere classified and limited to the skin Livedo vasculitis , capillaritis alba , erythema elevatum et diutinum -
L96 not forgiven - -
L97 Leg ulcer, not elsewhere classified Leg Ulcer -
L98 Other skin and subcutaneous diseases, not elsewhere classified Granuloma pediculatum ( Granuloma pyogenicum ), dermatitis factitia ( neurotic excoriation ), acute febrile neutrophilic dermatosis ( Sweet's syndrome ), eosinophilic cellulitis ( Wells syndrome ), tropic ulcer , mucinosis of the skin , focal mucinosis , lichen myxedematosus -
L99 * Other diseases of the skin and subcutaneous tissue in diseases classified elsewhere Cutaneous amyloidosis ( lichen amyloidosus , macular amyloidosis ) -

See also

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